In this educational exhibit we propose to achieve these objectives: To recognize the imaging appearance of cavernous transformation of portal vein; – To. While, ascites is a common sign in patients with POEMS, it is unfrequently associated with portal cavernomatosis and portal hypertension. We report a case of a. Rev Esp Enferm Dig. Mar;(3) Portal hydatid with secondary cavernomatosis. Rodríguez Sanz MB(1), Roldán Cuena MD(2), Blanco Álvarez.

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The treatment of the disease depends on the extension of plasma cells infiltration. Pellegrino 1S. Giambelluca 1M.

Their mycrobiological cultures and CRP for Mycobacterium tuberculosis and Histoplasma capsulatum were negative. Potral section showed hepatoesplenomegaly and a portal cavernoma and multiple tortuous vessels and ascites.

In conclusion, POEMS syndrome is an extremely rare disease and may include a wide variety of clinical manifestations. Partial pancreaticoduodenectomy England, due to unknown pancreatic disease.

A lower limbs electromyography was performed showing a sensitive-motor axonal polyneuropathy. Castleman disease, osteosclerotic inju ries and the elevated vascular endothelial growth factor VEGF. Typically these changes are:. Thoracic and abdominal computed tomography scan.


Dimarco 1G. Treatment with diuretics was started. The association with Castleman disease is generally related to a worse prognosis.

Haouari 3N. Bartolotta 1S. The diagnosis of POEMS syndrome is confirmed when the patient meets diagnostic criteria, which are classified into major and minor. Aldana Silva 1N. On physical examination, poratl abdominal ascites and hepatosplenomegaly was present only.

SONOWORLD : Portal cavernoma (cavernous transformation of the portal vein)

Case 5 Case 5. Dali 4A. MRI is usually reserved to clarify associated cabernomatosis hepatocellular nodules that may be seen in up to a fifth of the patients, particularly the focal nodular hyperplasia -like lesions 8.

After the initial evaluation, the patient experienced progressive deterioration over the following 4 months.

Learning objectives

Dimarco 1D. CTPV is most of the times inefficient in guaranteeing adequate portal vein inflow to the liver parenchyma far from the hilum and, therefore, is associated with an increased hepatic arterial flow to those peripheral liver segments. Bartolotta 1A. Case 2 Case 2. Pellegrino 1D. The authors declare that there are no conflicts of interest and there are no cavernomatosiss source.


In patients whose portal vein does not recanalize, or only partially re-canalizes, collateral veins thought to be paracholedochal veins dilate and become serpiginous. Case 1 Case 1. Personal information Silvia Pellegrino, silviapellegrino82 libero. ECR Poster No.: Cavernous Transformation of the Portal Vein: Caruana 1M.

Dimarco 1T. Case 9 Case 9. Check for errors and try again.

[Portal hypertension due to cavernomatosis of the portal vein].

Cavernous transformation of the portal vein CTPV is a sequela of portal vein thrombosis and is the replacement of the normal single channel portal cavernomatosus with numerous tortuous venous channels. Cavernous transformation appears as numerous tortuous vessels occupying the portal vein bed.

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